International Journal of Pediatric Otorhinolaryngology
Volume 73, Issue 12 , Pages 1682-1685 , December 2009

Cochlear abnormalities associated with enlarged vestibular aqueduct anomaly

  • Joseph S. Atkin

      Affiliations

    • University of Utah School of Medicine, UT, United States
    • Corresponding Author InformationCorresponding author. Tel.: +1 18018097027.
    • ,
  • J. Fredrik Grimmer

      Affiliations

    • Division of Otolaryngology, University of Utah, Primary Children's Medical Center, UT, United States
    • ,
  • Gary Hedlund

      Affiliations

    • Department of Radiology, Primary Children's Medical Center, UT, United States
    • ,
  • Albert H. Park

      Affiliations

    • Division of Otolaryngology, University of Utah, UT, United States

Received 6 May 2009 ,Revised 23 August 2009 ,Accepted 26 August 2009.

References 

  1. Mondini C. Minor works of Carlo Mondini: the anatomical section of a boy born deaf. Am. J. Otol. 1997;18(3):288–293
  2. Griffith A, Arts A, Downs C, Innis JW, Shepard NT, Sheldon S, et al. Familial large vestibular aqueduct syndrome. Laryngoscope. 1996;106(8):960–965
  3. Gussen R. The endolymphatic sac in the Mondini disorder. Arch. Otorhinolaryngol. 1985;242(1):71–76
  4. Kodama A, Sando I. Dimensional anatomy of the vestibular aqueduct and the endolymphatic sac (rugose portion) in human temporal bones. Statistical analysis of 79 bones. Ann. Otol. Rhinol. Laryngol. Suppl. 1982;96:13–20
  5. Kodama A, Sando I. Postnatal development of the vestibular aqueduct and endolymphatic sac. Ann. Otol. Rhinol. Laryngol. Suppl. 1982;96:3–12
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  8. Jackler R, De La Cruz A. The large vestibular aqueduct syndrome. Laryngoscope. 1989;99(12):1238–1242(discussion 1242–1243)
  9. Koesling S, Rasinski C, Amaya B. Imaging and clinical findings in large endolymphatic duct and sac syndrome. Eur. J. Radiol. 2006;57(1):54–62
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  11. Robson CD. Congenital hearing impairment. Pediatr. Radiol. 2006;36(4):309–324
  12. Grimmer JF, Hedlund G, Park A. Steroid treatment of hearing loss in enlarged vestibular aqueduct anomaly. Int. J. Pediatr. Otorhinolaryngol. 2008;72(11):1711–1715
  13. Grimmer JF, Hedlund G. Vestibular symptoms in children with enlarged vestibular aqueduct anomaly. Int. J. Pediatr. Otorhinolaryngol. 2007;71(2):275–282
  14. Harnsberger HR, Dahlen RT, Shelton C, Gray SD, Parkin JL. Advanced techniques in magnetic resonance imaging in the evaluation of the large endolymphatic duct and sac syndrome. Laryngoscope. 1995;105(10):1037–1042
  15. Sennaroglu L, Saatci I. A new classification for cochleovestibular malformations. Laryngoscope. 2002;112(12):2230–2241
  16. Albert S, Blons H, Jonard L, Feldmann D, Chauvin P, Loundon N, et al. SLC26A4 gene is frequently involved in nonsyndromic hearing impairment with enlarged vestibular aqueduct in Caucasian populations. Eur. J. Hum. Genet. 2006;14(6):773–779
  17. Becker TS, Vignaud J, Sultan A, Lachman M. The vestibular aqueduct in congenital deafness: evaluation by the axial projection. Radiology. 1983;149(3):741–744
  18. Emmett J. The large vestibular aqueduct syndrome. Am. J. Otol. 1985;6(5):387–415
  19. Mafee MF, Charletta D, Kumar A, Belmont H. Large vestibular aqueduct and congenital sensorineural hearing loss. AJNR Am. J. Neuroradiol. 1992;13(2):805–819
  20. Valvassori G, Clemis J. The large vestibular aqueduct syndrome. Laryngoscope. 1978;88(5):723–728

PII: S0165-5876(09)00465-0

doi: 10.1016/j.ijporl.2009.08.028

International Journal of Pediatric Otorhinolaryngology
Volume 73, Issue 12 , Pages 1682-1685 , December 2009

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